A case of glaucoma associated with Sturge-Weber syndrome and Nevus of Ota.

Lee,  H; Choi,  S S; Kim,  S S; Hong,  Y J

doi:2001.15.1.48

Korean J Ophthalmol > Volume 15(1); 2001 > Article

Case Report

Korean Journal of Ophthalmology 2001;15(1):48-53.
DOI: https://doi.org/10.3341/kjo.2001.15.1.48 Published online June 30, 2001.

A case of glaucoma associated with Sturge-Weber syndrome and Nevus of Ota.

H Lee, S S Choi, S S Kim, Y J Hong

The Institute of Vision Research, Department of Ophthalmology, Yonsei University College of Medicine, Seoul, Korea.

Abstract

The Sturge-Weber syndrome consists of a unilateral port-wine hemangioma of the skin along the trigeminal distribution and is accompanied by an ipsilateral leptomeningeal angioma. Glaucoma is present in approximately half of the cases. The Nevus of Ota is a melanocytic pigmentary disorder, most commonly involving the area innervated by the trigeminal nerve. Elevated intraocular pressure, with or without glaucomatous damage, is observed in 10% of the cases. We report the first case of glaucoma associated with Sturge-Weber syndrome and Nevus of Ota in Korea.